Beta-Thalassemia
unseel.com · alpha excess  ·  ineffective erythropoiesis  ·  HbA2 > 3.5%
α:β ratio 1.0
stage balanced
HbA2 2.5%
state
Alpha-globin chains (unchanged output)
Beta-globin chains (HBB-encoded)
HbA2 / HbF diagnostic rise
Precipitated alpha · dying precursors
Unseel.com · Beta-Thalassemia: When the Globin Chains Don't Balance