Congenital Adrenal Hyperplasia
unseel.com · the 21-hydroxylase (CYP21A2) block
17-OHP 80 ng/dL
ACTH normal
arm resting
state
Steroid precursors (cholesterol → 17-OHP)
Aldosterone & cortisol (blocked arms)
21-hydroxylase block · androgen shunt
ACTH drive → adrenal hyperplasia
Unseel.com · Congenital Adrenal Hyperplasia: The 21-Hydroxylase Block